Caring for a person with cystic fibrosis.

Cystic Fibrosis (CF) is Irelands most common genetically inherited disorder. CF was once thought of as a childhood illness, however, therapeutic advances and more effective treatment modalities have resulted in many children with CF living into adulthood. Nurses are in prime positions to provide support for parents particularly at the diagnosis stage. Because of the chronic nature of CF, a long relationship is often formed between the nurse, the child and their family. This literature review presents current CF screening and diagnostic trends as well as examining the importance of early intervention. Non-compliance with the complex treatment regime for CF remains the biggest challenge facing the CF medical teams. This review explores the many factors to consider when planning interventions to increase compliance. Because of increasing life expectancy, the quality of life of people with CF has become an important therapeutic consideration. This literature review examines the psychological well being of these individuals. The development of dedicated CF units allow the provision high quality care which means the future is brighter than ever before for people with CF.